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Incidental finding of pulmonary arterial sling during patent ductus arteriosus surgery in a patient with Mowat–Wilson syndrome

Part of: Cardiac Morphology

Published online by Cambridge University Press:  29 June 2018

Juan D. Cano Sierra Open the ORCID record for Juan D. Cano Sierra [Opens in a new window] ,
Camilo F. Mestra  and
Miguel A. Ronderos Dumit
Juan D. Cano Sierra*
Affiliation:
Pediatric Cardiology Hospitalist, Fundación Cardioinfantil, Bogotá, Colombia
Camilo F. Mestra
Affiliation:
Pediatric Cardiology Department, Universidad Del Rosario, Bogotá, Colombia
Miguel A. Ronderos Dumit
Affiliation:
Pediatric Interventional Cardiology Department, Fundación Cardioinfantil, Bogotá, Colombia
*
Author for correspondence: J. D. Cano Sierra, Pediatric Cardiology Hospitalist, Fundación Cardioinfantil, Cl. 163a #13B-60, Bogotá, Colombia. Tel: +057 318 209 8921; Fax: +057 667 2737; E-mail: csdavid0413@gmail.com
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Abstract

Mowat–Wilson syndrome is a genetic condition due to a mutation in the ZEB2 gene; it affects many systems including the cardiovascular system. The pulmonary arterial sling originates from a failure of development of the proximal portion of the left sixth aortic arch, resulting in an anomalous left pulmonary artery origin from the posterior wall of the right pulmonary artery and the left pulmonary artery crossing to the left lung between the trachea and the oesophagus. We present a 4-month-old infant with Mowat–Wilson syndrome and left pulmonary arterial sling, and discuss the association of these two rare conditions. Pulmonary arterial sling is significantly more frequent in patients with Mowat–Wilson syndrome than in the general population.

Keywords

Mowat–Wilson syndrome6th aortic archZEB2pulmonary arterial slinggeneral cardiology
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 8 , August 2018 , pp. 1074 - 1076
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Copyright
© Cambridge University Press 2018 

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Footnotes

Cite this article: Cano Sierra JD, Mestra CF, Ronderos Dumit MA. (2018) Incidental finding of pulmonary arterial sling during patent ductus arteriosus surgery in a patient with Mowat–Wilson syndrome. Cardiology in the Young28: 1074–1076. doi: 10.1017/S1047951118000689

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