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Degenerative Progressive Myoclonic Epilepsy Electrokymographic Observations

Published online by Cambridge University Press:  18 September 2015

Iraj Derakhshan ,
Jamshid Lotfi  and
Kazem Abbsssioun
Iraj Derakhshan*
Affiliation:
Departments of Neurology and Neuro-surgery, Dariush-Kabir Medical School, Tehran University, Tehran, Iran
Jamshid Lotfi
Affiliation:
Departments of Neurology and Neuro-surgery, Dariush-Kabir Medical School, Tehran University, Tehran, Iran
Kazem Abbsssioun
Affiliation:
Departments of Neurology and Neuro-surgery, Dariush-Kabir Medical School, Tehran University, Tehran, Iran
*
1670 Sheridan Road, South Euclid, Ohio 44121 U.S.A.
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Summary

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Clinical and pathological findings in two cases of degenerative progressive myoclonic epilepsy (PME) are described. The clinically difficult task of differentiating a “cerebellar” tremor from an action myoclonus is emphasized. Simultaneous elect roencephalography and electrokymography was done, using capacity to ground transients for recording hand movements. This method was found useful in corroborating the cerebellar nature of the remaining disorder, after successful treatment of the myoclonic element with anticonvulsants.

Type
Research Article
Information
Canadian Journal of Neurological Sciences , Volume 6 , Issue 1 , February 1979 , pp. 65 - 68
Copyright
Copyright © Canadian Neurological Sciences Federation 1979

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