Hostname: page-component-78c5997874-lj6df Total loading time: 0 Render date: 2024-11-18T07:42:37.902Z Has data issue: false hasContentIssue false

Primary-care management of patients with congenital anomalies of the coronary arteries*

Published online by Cambridge University Press:  16 December 2015

Jeffrey R. Boris*
Affiliation:
Children’s Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
Julie A. Brothers
Affiliation:
Children’s Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
*
Correspondence to: Dr J. R. Boris, MD, Division of Cardiology, Children’s Hospital of Philadelphia, 3401 Civic Center Boulevard, Philadelphia, PA 19104, United States of America. Tel: 215-590-3180; Fax: 267-426-5324; E-mail: borisj@email.chop.edu

Abstract

Congenital anomalies of the coronary arteries, although uncommon, have the potential to cause serious myocardial damage, ischaemic cardiomyopathy, and sudden cardiac death. This article summarises aspects of care for these patients in the outpatient setting, including clinical history and physical examination findings, ancillary testing, decision-making regarding the need for surgical intervention, and recommendations for physical activity. Although there are limited data regarding some of these recommendations, it is hoped that these can be used as an initial benchmark against which further data will lead to a more evidence-based approach.

Type
Original Articles
Copyright
© Cambridge University Press 2015 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Footnotes

*

Presented at the Johns Hopkins All Children’s Heart Institute’s 15th Annual International Symposium on Congenital Heart Disease, Saint Petersburg, Florida, United States of America, from Friday, 6 February, 2015 to Monday, 9 February, 2015.

References

1.Gross, RE. Surgical management of the patent ductus arteriosus with summary of four surgically treated cases. Ann Surg 1939; 110: 321356.CrossRefGoogle ScholarPubMed
2.Wernovsky, G, Rome, JJ, Tabbutt, S, et al. Guidelines for the outpatient management of complex congenital heart disease. Congenit Heart Dis 2006; 1: 1026.CrossRefGoogle ScholarPubMed
3.Boris, JR. Primary care cardiology for patients with hypoplastic left heart syndrome. Cardiol Young 2011; 21 (Suppl 2): 5358.CrossRefGoogle ScholarPubMed
4.Boris, JR. Primary care management of patients with common arterial trunk and transposition of the great arteries. Cardiol Young 2012; 22: 781787.CrossRefGoogle ScholarPubMed
5.Boris, JR. Primary cardiovascular care for patients with valvar cardiac disease. Cardiol Young 2014; 24: 10571063.CrossRefGoogle ScholarPubMed
6.Bland, EF, White, PD, Garland, J. Congenital anomalies of the coronary arteries: report of an unusual case associated with cardiac hypertrophy. Am Heart J 1933; 8: 787801.CrossRefGoogle Scholar
7.Kimball, TR. Pediatric stress echocardiography. Pediatr Cardiol 2002; 23: 347357.CrossRefGoogle ScholarPubMed
8.Wood, S, Thompson, WR. Exercise stress echocardiography in children at risk for coronary artery insufficiency rarely detects new regional wall motion abnormalities. Poster session presented at: Johns Hopkins All Children’s Heart Institute 15th International Symposium on Congenital Heart Disease; February 6–9, 2015, St. Petersburg, FL.Google Scholar
9.Roberts, WC. Major anomalies of coronary arterial origin seen in adulthood. Am Heart J 1986; 111: 941963.CrossRefGoogle ScholarPubMed
10.Taylor, AJ, Rogan, KM, Virmani, R. Sudden cardiac death associated with isolated congenital coronary anomalies. J Am Coll Cardiol 1992; 20: 640647.CrossRefGoogle Scholar
11.Frescura, C, Basso, C, Thiene, G, et al. Anomalous origin of coronary arteries and risk of sudden death: a study based on an autopsy population of congenital heart disease. Hum Pathol 1998; 29: 689695.CrossRefGoogle Scholar
12.Said, SA, Lam, J, van der Werf, T. Solitary coronary artery fistulas: a congenital anomaly in children and adults. A contemporary review. Congenit Heart Dis 2006; 1: 6376.CrossRefGoogle ScholarPubMed
13.Ceresnak, S, Gray, RG, Altmann, K, et al. Congenit Heart Dis 2007; 2: 208213.CrossRefGoogle Scholar
14.Angelini, P. Congenital coronary ostial disease: a spectrum of anatomic variants with different pathophysiologies and prognoses. Tex Heart Inst J 2012: 3955-9.Google ScholarPubMed
15.Maron, BJ, Zipes, DP. 36th Bethesda Conference. Eligibility recommendations for competitive athletes with cardiovascular abnormalities. J Am Coll Cardiol 2005; 45: 13261333.CrossRefGoogle Scholar
16.Laureti, JM, Singh, K, Blankenship, J. Anomalous coronary arteries: a familial clustering. Clin Cardiol 2005; 28: 488490.CrossRefGoogle ScholarPubMed
17.Horan, PG, Murtagh, G, McKeown, PP. Single coronary artery: a familial clustering. Heart 2003; 89: e27.CrossRefGoogle ScholarPubMed
18.Bunce, NH, Rahman, SL, Keegan, J, Gatehouse, PD, Lorenz, CH, Pennelli, DJ. Anomalous coronary arteries: anatomic and functional assessment by coronary and perfusion cardiovascular magnetic resonance in three sisters. J Cardiovasc Magn Reson 2001; 3: 361369.CrossRefGoogle ScholarPubMed
19.Wilson, W, Taubert, KA, Gewitz, M, et al. Prevention of infective endocarditis: guidelines from the American Heart Association: a guideline from the American Heart Association Rheumatic Fever, Endocarditis, and Kawasaki Disease Committee; American Heart Association Council on Cardiovascular Disease in the Young; American Heart Association Council on Clinical Cardiology; American Heart Association Council on Cardiovascular Surgery and Anesthesia; Quality of Care and Outcomes Research Interdisciplinary Working Group. Circulation 2007; 116: 17361754.CrossRefGoogle Scholar
20.Brothers, JA, Gaynor, JW, Jacobs, JP, et al. The registry of anomalous aortic origin of the coronary artery of the Congenital Heart Surgeons’ Society. Cardiol Young 2010; 20 (Suppl 3): 5058.CrossRefGoogle ScholarPubMed