Canadian Journal of Neurological Sciences: Volume 4 -

Myopathy Associateci with Amyloid Angiopathy
Joseph Bruni, Juan M. Bilbao, Kenneth P. H. Pritzker
Published online by Cambridge University Press:

03 July 2018, pp. 77-80
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A 38-year-old patient with the clinical picture of a progressive myopathy resembling limb girdle muscular dystrophy is presented. Muscle biopsy showed amyloid deposits in the walls of small endomysial blood vessels. There was no clinical or physiological evidence of peripheral nerve involvement, no plasma cell dyscrasia and no generalized amyloidosis. There was no muscle fiber hypertrophy, inflammation or neurogenic change. There was no response to steroid therapy.
The etiopathogenesis of this amyloid angiopathy is undetermined. The extensive vessel involvement with amyloid deposition and the absence of changes indicative of muscular dystrophy or inflammatory myopathy leads us to favor an ischemic basis for this patient’s myopathy.

Index to Volume 4
Published online by Cambridge University Press:

18 September 2015, pp. (i)-(xii)
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Announcements
Published online by Cambridge University Press:

18 September 2015, pp. (xiv)-(xvi)
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Canadian Journal of Neurological Sciences