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Chapter 29 - Iron Storage Disorders in Children

from Section IV - Metabolic Liver Disease

Published online by Cambridge University Press:  19 January 2021

By
Sarah A. Taylor ,
Michael R. Narkewicz  and
Cara L. Mack
Edited by
Frederick J. Suchy ,
Ronald J. Sokol  and
William F. Balistreri
Edited in association with
Jorge A. Bezerra ,
Cara L. Mack  and
Benjamin L. Shneider
Frederick J. Suchy
Affiliation:
University of Colorado, Children’s Hospital Colorado, Aurora
Ronald J. Sokol
Affiliation:
University of Colorado, Children’s Hospital Colorado, Aurora
William F. Balistreri
Affiliation:
Cincinnati Children’s Hospital Medical Center, Cincinnati
Jorge A. Bezerra
Affiliation:
Cincinnati Children’s Hospital Medical Center, Cincinnati
Cara L. Mack
Affiliation:
University of Colorado, Children’s Hospital Colorado, Aurora
Benjamin L. Shneider
Affiliation:
Texas Children’s Hospital, Houston
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Summary

Iron overload states can be classified as primary or secondary. There are many disorders that can lead to iron overload (Table 29.1) [1, 2]. This chapter focuses on hereditary hemochromatosis (HH), juvenile hemochromatosis (JHH), and secondary iron overload (primarily transfusion associated) in the pediatric patient and in neonatal hemochromatosis (NH).

Type
Chapter
Information
Liver Disease in Children , pp. 515 - 529
Publisher: Cambridge University Press
Print publication year: 2021

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