SJÖGREN's syndrome is a presumably autoimmune disease with parthologic findings of lymphocytic infiltration of the involved structures. Although the salivary and lacrimal gl ands are the most commonly involved sites, extragl andular lymphoproliferation also occurs. Upper and lower respiratory tract lymphoproliferation is known, but only one case of Sjögren's disease of the larynx has been previously reported. We present a case of laryngeal involvement in which the gross pathologic appearance is different from that in the earlier case report. The otolaryngologist should consider Sjögren's disease in the differential diagnosis of diffuse laryngeal lesions.