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Sepsis from Neurofibromatosis

Published online by Cambridge University Press:  02 December 2014

Navdeep Tangri*
Affiliation:
Department of Internal Medicine, McGill University, Montreal, Quebec, Canada
Shireen Sirhan
Affiliation:
Department of Internal Medicine, McGill University, Montreal, Quebec, Canada
Gordon Crelinsten
Affiliation:
Department of Internal Medicine, McGill University, Montreal, Quebec, Canada
*
Department of Internal Medicine, McGill University, 1209 - 4870 Ch Cote Des Neiges, Montreal, Quebec, H3V 1H3, Canada
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Neurofibromatosis Type I or von Recklinghausen’s neurofibromatosis is an autosomal dominant disorder with a high index of spontaneous mutations and extremely varied and unpredictable clinical manifestations. We present a case of sepsis secondary to an infected hematoma, enclosed within a massive neurofibroma.

A 42-year-old man presented to the emergency department with a one week history of fever and chills. He reported an increase in pain and size of a growth near his chest. The patient was noted to be febrile on arrival. On physical examination, a very large neurofibroma was seen extending from the right upper chest. Wound and blood cultures were obtained. Computed Tomography (CT) of the thorax revealed a hematoma contained within the large mass.

Type
Peer Reviewed Letter
Copyright
Copyright © The Canadian Journal of Neurological 2006

References

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