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Attentional and Perseverative Impairment in Two Cases of Familial Fatal Parkinsonism with Cortical Sparing

Published online by Cambridge University Press:  18 September 2015

D. Kimura ,
A. Hahn  and
H.J.M. Barnett
D. Kimura*
Affiliation:
Department of Psychology and the Department of Clinical Neurological Sciences, University of Western Ontario, London
A. Hahn
Affiliation:
Department of Psychology and the Department of Clinical Neurological Sciences, University of Western Ontario, London
H.J.M. Barnett
Affiliation:
Department of Psychology and the Department of Clinical Neurological Sciences, University of Western Ontario, London
*
Department of Psychology, University of Western Ontario, London, Ontario, Canada N6A 5C2
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Abstract:

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The neuropsychological findings in twin brothers with familial fatal Parkinsonism are reported. Post-mortem examination had shown extensive pathology in basal ganglia and brainstem, but not in the cerebral cortex. Although both showed average intelligence three months prior to death, they had impairment on a sorting task and in serial attention span. Some possible neural mechanisms are discussed.

Type
Original Articles
Information
Canadian Journal of Neurological Sciences , Volume 14 , Issue 4 , November 1987 , pp. 597 - 599
Copyright
Copyright © Canadian Neurological Sciences Federation 1987

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