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La dystrophie myotonique: I caractéristiques socio-économiques et résidentielles des malades

Published online by Cambridge University Press:  18 September 2015

Michel Perron
Affiliation:
Du départment de Travail social, CÉGEP de Jonquière
Suzanne Veillette
Affiliation:
département de Sciences humaine, CÉGEP de Jonquière, San Francisco
Jean Mathieu
Affiliation:
la Clinique de dystrophie musculaire, Hôpital de Chicoutimi
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Abstract:

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Myotonic Dystrophy: I Socio-Economic and Home-Environment Characteristics of the Patients. Myotonic dystrophy is a dominantly inherited genetic disorder which, in medical literature, has been linked to peculiar socio-economical conditions. In order to document this assertion, a sociological study was conducted in the Saguenay-Lac-Saint-Jean region (Quebec), using a representative sample (N = 218) drawn from the myotonic dystrophy population. A study of the patients' places of residence was also carried out. The results clearly indicate that myotonic dystrophy patients exhibit a socio-economic profile associated with disadvantaged milieux: high unemployment, low income and limited schooling. Many of these patients must rely on social welfare. Two families out of five (42%) live beneath the poverty line. The wage-earning history of these persons is closely linked to their self-evaluation of their working capabilities. After the age of forty, a high proportion of these people are unable to hold down a paying job and claim they are unable to do so. Within a well-screened urban area, a study of the patients' places of residence indicates census tracts where myotonic dystrophy is concentrated (ecological niches). These social areas are close to the downtown area and display characteristics of disadvantaged milieux. Accordingly, the My D gene seems to be confined to a specific socio-economic and socio-geographical environment, through which the spread of the gene is channelled among the population.

Type
SPECIAL SUPPLEMENT Dystrophie myotonique au Québec
Copyright
Copyright © Canadian Neurological Sciences Federation 1989

References

1.Benoist, J. La dynamique biosociale. Présentation. Anthropologie et sociétés 1981; 5 (2): 13.CrossRefGoogle Scholar
2.Billette, A. Les inégalités sociales de mortalité au Québec. Recherches sociographiques 1977; 18 (3): 415430.CrossRefGoogle Scholar
3.Enquête Santé Canada. La santé des canadiens. Ottawa: Approvisionnements et services 1981.Google Scholar
4.Conseil national du bien-être social. Les pauvres et les soins de santé au Canada. Ottawa: Approvisionnements et Services 1982.Google Scholar
5.Adiê, WJ, Greenfield, JG. Dystrophia Myotonica (Myotonia Atrophica). Brain 1923; 46: 73127.CrossRefGoogle Scholar
6.Thomasen, E. Myotonia. Denmark: Aarhuus Stiftsbogtrykkerie 1948: 161162.Google Scholar
7.Caughey, JE, Myrianthopoulos NC: Dystrophia myotonica and related disorders. Springfield: Charles C. Thomas 1963: 120122.Google Scholar
8.Harper, PS, Saunders, WB. Myotonic dystrophy. Philadelphia 1979: 33, 142143.Google Scholar
9.Mathieu, J, Simard, M, De Braekeleer, M, et al. Partial syndrome of myotonic dystrophy: clinical présentation and follow-up. Can J Neurol Sci 1989; 99103.CrossRefGoogle ScholarPubMed
10.Lee, TR. Race and Residence. The concentration and dispersion of immigrants in London. Londres: Oxford University Press 1977: 171172.Google Scholar
11.Foggin, P, Desmarais, L, Joly, MF, et al. Analyse cartographique de la morbiditè hospitalire dans l’Île de Montreal. Cahiers de géographie du Québec 1983; 27: 185208.CrossRefGoogle Scholar
12.Bemèche, F, Martin, JC. Immigration, emploi et logement: la situa-tion de la population haïtienne dans certaines Eones de la rgégion métropolitaine de Montréal. Anthropologie et sociétés 1984; 8: 529.Google Scholar
13.Statistique Canada. Enquête sur la population active. Ottawa: Approvisionnements et Services 1984.Google Scholar
14.Statistique Canada. Recensement de la population. Ottawa: Approvisionnements et Services 1982; catalogue 95942.Google Scholar
15.Conseil national de bien-Eare social. Les seuils de pauvreté de 1985. Ottawa: Approvisionnements et Services 1985: 7.Google Scholar
16.Veillette, S, Perron, M, Desbiens, F. La dystrophie myotonique: étude épidémiologique et socio-géographique au Saguenay-Lac-Saint-Jean. Jonquière: Cégep de Jonquière, rapport de recherche 1986: 158177.Google Scholar
17.Loslier, L. La mortalité dans les aires sociales de la région métropolitaine de Montréal. Québec: Ministère des Affaires sociales, 1976.Google Scholar
18.Lalouel, JM. Concentrations locales d’affections héréditaires rares. Paris: L’Expansion 1970.Google Scholar
19.Plauchu, H, Bideau, A. Epidémiologie et constitution d’un registre de population à propos d’une concentration géographique d’une maladie héréditaire rare. Population 1984; 4–5: 765786.CrossRefGoogle Scholar
20.Picheral, H. Espace et santé. Géographie médicale du Midi de la France. Montpellier: Imprimerie du Paysan du Midi 1976.Google Scholar
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