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Hydrocephalus and Headaches in Paget’s Disease of the Skull: Complete Relief by Ventriculo-Atrial Shunt

Published online by Cambridge University Press:  18 September 2015

Chantal Hausser ,
Georges Elie Ouaknine  and
Jacques Sylvestre
Chantal Hausser
Affiliation:
Divisions of Neurology, Neurosurgery and Radiology, Hôtel-Dieu de Montréal and Université de Montréal
Georges Elie Ouaknine
Affiliation:
Divisions of Neurology, Neurosurgery and Radiology, Hôtel-Dieu de Montréal and Université de Montréal
Jacques Sylvestre
Affiliation:
Divisions of Neurology, Neurosurgery and Radiology, Hôtel-Dieu de Montréal and Université de Montréal
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Summary

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A 76 year old patient with a long history of headaches was found to have Paget’s disease and communicating hydrocephalus. There were (otherwise) no neurological or musculo-skeletal manifestations of Paget’s disease, but moderate impairment of intellectual function was present. Treatment with disphosphonates did not bring any significant improvement, but three days following a ventriculo-atrial shunting procedure, the patient became headache-free for the first time in several years.

In the literature, patients with hydrocephalus have been shown to respond quite unevenly to atrio-ventricular shunting, but in most instances the descriptions concerned advanced cases with well-established symptoms of dementia, ataxia and incontinence. Our case is reported to stress the importance of early diagnosis and management of hydrocephalus in Paget’s disease for the prevention of widespread neurological dysfunction.

Type
Original Articles
Information
Canadian Journal of Neurological Sciences , Volume 11 , Issue 1 , February 1984 , pp. 69 - 72
Copyright
Copyright © Canadian Neurological Sciences Federation 1984

References

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