Book contents
- Respiratory Disease in Pregnancy
- Respiratory Disease in Pregnancy
- Copyright page
- Contents
- Contributors
- Section 1 The Basics: for the Obstetrician
- Section 2 The Basics: for the Non-Obstetrician
- Section 3 Pulmonary Conditions Not Specific to Pregnancy
- 6 Pulmonary Infections in Pregnancy
- 7 Asthma in Pregnancy
- 8 Cystic Fibrosis in Pregnancy
- 9 Restrictive Lung Disease in Pregnancy
- 10 Thromboembolic Disease in Pregnancy
- 11 Pulmonary Hypertension and Pregnancy
- 12 Sickle Chest Syndromes in Pregnancy
- 13 Sleep-disordered Breathing in Pregnancy
- 14 Acute Respiratory Distress Syndrome in Pregnancy
- 15 Other Pulmonary Conditions in Pregnancy: Pleural Disease, Haemoptysis and Air Embolism
- Section 4 Pulmonary Conditions Related to Pregnancy
- Section 5 Other Pulmonary Issues in Pregnancy
- Index
- References
8 - Cystic Fibrosis in Pregnancy
from Section 3 - Pulmonary Conditions Not Specific to Pregnancy
Published online by Cambridge University Press: 14 April 2020
Book contents
- Respiratory Disease in Pregnancy
- Respiratory Disease in Pregnancy
- Copyright page
- Contents
- Contributors
- Section 1 The Basics: for the Obstetrician
- Section 2 The Basics: for the Non-Obstetrician
- Section 3 Pulmonary Conditions Not Specific to Pregnancy
- 6 Pulmonary Infections in Pregnancy
- 7 Asthma in Pregnancy
- 8 Cystic Fibrosis in Pregnancy
- 9 Restrictive Lung Disease in Pregnancy
- 10 Thromboembolic Disease in Pregnancy
- 11 Pulmonary Hypertension and Pregnancy
- 12 Sickle Chest Syndromes in Pregnancy
- 13 Sleep-disordered Breathing in Pregnancy
- 14 Acute Respiratory Distress Syndrome in Pregnancy
- 15 Other Pulmonary Conditions in Pregnancy: Pleural Disease, Haemoptysis and Air Embolism
- Section 4 Pulmonary Conditions Related to Pregnancy
- Section 5 Other Pulmonary Issues in Pregnancy
- Index
- References
Summary
Cystic fibrosis (CF) is an autosomal recessive genetic disorder caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene that results in a multisystem disease. CF most commonly affects the respiratory, hepatobiliary, digestive and reproductive systems, though the majority of morbidity and mortality results from progressive obstructive lung disease and chronic pulmonary infection. In recent years, the survival of patients with CF has increased significantly with a recently reported median survival of up to 51.8 years of age.
- Type
- Chapter
- Information
- Respiratory Disease in Pregnancy , pp. 73 - 81Publisher: Cambridge University PressPrint publication year: 2020
References
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