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Nasal haemophilic pseudotumour

Published online by Cambridge University Press:  29 June 2007

P. Raj*
Affiliation:
Department of Otolaryngology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
J. T. Wilde
Affiliation:
Department of Haematology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
J. Oliff
Affiliation:
Department of Radiology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
A. B. Drake-Lee
Affiliation:
Department of Otolaryngology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
*
Address for correspondence: Mr P. Raj, 44 Humphrey Middlemore Drive, Harborne, Birmingham B17 0JN.

Abstract

Haemophilic pseudotumour or haemophilic cyst is a rare complication of haemophilia, occurring in one to two per cent of individuals with a severe factor VIII or IX deficiency. We report a case of a haemophilic pseudotumour in a hitherto unreported site, the bony nasal pyramid, and believe this case is also unique on account of it having occurred in a patient with mild haemophilia. The diagnosis and treatment of this rare condition is also reviewed.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1999

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