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Klippel-Feil syndrome and conductive deafness

Published online by Cambridge University Press:  29 June 2007

Eleanor J. Stewart*
Affiliation:
Glasgow
B. F. O'Reilly
Affiliation:
Glasgow
*
Miss E. J. Stewart, FRCS, ENT Department, Stobhill General Hospital, Glasgow G21 3UW.

Abstract

The Klippel-Feil syndrome is usually associated with sensorineural deafness and reports of conductive or mixed deafness are rare. Four additional cases are presented in this paper. The middle ear anomalies found in this syndrome are discussed. The results of middle ear surgery are reviewed and found to be poor.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1989

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References

Clarke, J. J. 1906 Lancet, 2: 1349.Google Scholar
Daniilidis, J., Maganaris, T. and Dimitriadis, A. (1978) Stapes gusher and Klippel-Feil syndrome. Laryngoscope, 88: 11781183.Google Scholar
Edwards, W. G. (1964) Congenital middle ear deafness with anomalies of the face. Journal of Laryngology and Otology, 74: 152170.CrossRefGoogle Scholar
Feil, A. (1919) L'absence et la Diminution des Vetebres cervicales. Paris Librairie Litteraire et Medicale, Paris 1919.Google Scholar
Glasscock, M. E. (1973) The stapes gusher. Archives of Otolaryngology, 98: 8291.CrossRefGoogle ScholarPubMed
Jalladeau, J. (1936) Malformations congenitales associees au syndrome del Klippel-Feil. These, Paris.Google Scholar
Jarvis, J. F. and Sellars, S. L. (1974) Klippel-Feil deformity associated with congenital conductive deafness. Journal of Laryngology and Otology, 88: 285289.Google Scholar
Klippel, M. and Feil, A. (1912) Un cas d'absence des vertebres cervicales avec cage thoracique remontent justu'a la base du crane. Novelle Inconographic de las Salpetriere 25: 223–250.Google Scholar
Sakai, M., Hirosater, M., Shinkawa, A. and Komatsu, N. (1983) Klippel-Feil syndrome with conductive deafness and histological findings of removed stapes. Annals of Otology, Rhinology and Laryngology, 92: 202205.Google Scholar
Singh, S. P., Rock, E. M. and Shulman, A. (1969) Klippel-Feil syndrome with unexplained apparent conductive hearing loss. A case report. Laryngoscope, 79: 113117.Google Scholar
Wildervanck, L. S. (1952). Een geval van aandvening van Klippel-Feil gecombineerd mel abducens paralyse, retractio bulbi en doofstemheid. Nederlands Tijdschrift voor Geneesk unde 96: 2752.Google Scholar
Windle-Taylor, P. C., Emery, P. J. and Phelps, P. D. (1981) Ear deformities associated with the Klippel-Feil syndrome. Annals of Otology, Rhinology and Laryngology, 90: 210216.Google Scholar