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Hyperacusis and Williams syndrome

Published online by Cambridge University Press:  29 June 2007

Ajay Nigam  and
Peter R. Samuel
Ajay Nigam
Affiliation:
Department of Otolaryngology, Royal Infirmary, Sunderland.
Peter R. Samuel*
Affiliation:
Department of Otolaryngology, Royal Infirmary, Sunderland.
*
Mr P.R. Samuel, F.R.C.S.E., Dalkeith Lodge, Aykley Heads Farm, Durham DH1 5AN.
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Abstract

Abnormal sensitivity to environmental sounds is a short-term feature often observed following insertion of grommets. Here we describe a child with this symptom who was found to have Williams syndrome, a condition in which hyperacusis is observed in 95 per cent of patients.

Keywords

Middle ear ventilationHyperacusis
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 108 , Issue 6 , June 1994 , pp. 494 - 496
Copyright
Copyright © JLO (1984) Limited 1994

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