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Failure to control the airway in a patient with Hunter's syndrome

  • Luis Gaitini (a1), Milo Fradis (a1), Sonia Vaida (a1), Geoffrey Collins (a1), Millian Croitoru (a1), Mustafa Somri (a1), Zvi Borochovltz (a1) and Avishai Golz (a1)...

Abstract

Hunter's syndrome is due to recessively inherited mucopolysaccharide storage diseases. The anaesthetic complications in this syndrome are related to the organs involved in the disease, but pertain especially to upper airway obstruction problems. We report a patient with Hunter's syndrome who, while under general anaesthesia for a simple procedure (the introduction of bilateral grommets), suffered a fatal outcome.

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Corresponding author

Address for correspondence: Milo Fradis, M.D., Department of Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, P.O.B. 4940, 31048 Haifa, Israel.

References

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