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Bilateral and multicystic major salivary gland disease: a rare presentation of primary Sjögren's syndrome

Published online by Cambridge University Press:  29 June 2007

Ijaz Ahmad*
Affiliation:
Department of Otolaryngology, Dudley Group of Hospitals, Russells Hall Hospital, Dudley, West Midlands, UK.
J. Ray
Affiliation:
Department of Otolaryngology, Dudley Group of Hospitals, Russells Hall Hospital, Dudley, West Midlands, UK.
R. J. Cullen
Affiliation:
Department of Otolaryngology, Dudley Group of Hospitals, Russells Hall Hospital, Dudley, West Midlands, UK.
R. T. J. Shortridge
Affiliation:
Department of Otolaryngology, Dudley Group of Hospitals, Russells Hall Hospital, Dudley, West Midlands, UK.
*
Address for correspondence: Ijaz Ahmad, F.R.C.S., Department of Otolaryngology, Russells Hall Hospital, Dudley DY1 2HQ. Fax: 01384 244169

Abstract

We present a case of a 15-year-old girl with bilateral parotid and sub-mandibular salivary gland enlargement as the sole presentation of primary Sjögren's syndrome. The clinical, radiological, immunological and pathological features have been discussed. The relevant literature has been reviewed. To our knowledge this is the only reported case of Sjögren's syndrome presenting as multicystic disease with bilateral major salivary gland involvement.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1998

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