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Otolaryngological manifestation of Gorlin Goltz syndrome

Published online by Cambridge University Press:  29 June 2007

Fatma Homood Al-Anazy  and
Siraj M. Zakzouk
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Abstract

A 46-year-old Jordanian man was seen in ENT clinic complaining of progressive left nasal obstruction and hearing loss for the last five years with a history of multiple surgical removal of dental cysts. Clinical and radiological investigation revealed a cystic mass occupying the left maxillary sinus protruding to the nasal cavity, calcification of the falx cerebri and bifid ribs. On these findingsGorlin-Goltz syndrome was confirmed. The case is presented and the literature reviewed.

Keywords

Basal cell naevus syndromeOtorhinolaryngology
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 111 , Issue 3 , March 1997 , pp. 286 - 289
Copyright
Copyright © JLO (1984) Limited 1997

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