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Valve-Sparing Replacement of the Aortic Root for a 2-year-old Child with Loeys-Dietz Syndrome

  • Yoshio Ootaki (a1), Minhaz Uddin (a1) and Ross M. Ungerleider (a1)


Loeys-Dietz syndrome is a newly recognized constellation that presents with aortic aneurysm or dissection similar to Marfan’s syndrome. We describe successful surgical treatment in a 2-year-old with the syndrome in whom we performed a valve-sparing replacement of the aortic root because of significant dilation of the aortic root and the ascending aorta.


Corresponding author

Correspondence to: Dr Ross Ungerleider, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: 216-844-3058; Fax: 216-844-3517; E-mail:


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