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Successful one stage biventricular correction of aortic atresia with a ventricular septal defect and discordant ventriculo-arterial connections

  • Tjark Ebels (a1), Friedhelm Dapper (a2), Jurgen Bauer (a3), Rainer M. Bohle (a4), Karl J. Hagel (a3), Peter G.J. Nikkels (a5) and Friedrich W. Hehrlein (a2)...

Summary

Aortic atresia is rare in the setting of a normally developed left ventricle with a ventricular septal defect. In this combination, as far as we know, it has been described only with concordant ventriculo-arterial connections, for which seven one-stage biventricular repairs have now been described. We describe here the case of a 3½-month-old male infant with a similar combination but with discordant ventriculo-arterial connections and severe pulmonary hypertension. It was the right ventricle which achieved normal size in this arrangement, presumably because of the ventricular septal defect. One-stage biventricular correction was accomplished, employing a single pulmonary allograft, aided by massive doses of Prostaglandin El. As far as we know this is the first report of the combination of aortic atresia, discordant ventriculo-arterial connections, a ventricular septal defect and balanced ventricles. We complement our surgical account, nonetheless, with a description of a comparable specimen from our anatomic museum.

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Corresponding author

Tjark Ebels MD PhD. Division of Cardiothoracic Surgery, Thorax Centrum, Academisch Ziekenhuis, P.O Box 30 001, 9700RB Groningen, The Netherlands. Tel: 31 50 3613238, Fax: 31 50 3611347

References

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Keywords

Successful one stage biventricular correction of aortic atresia with a ventricular septal defect and discordant ventriculo-arterial connections

  • Tjark Ebels (a1), Friedhelm Dapper (a2), Jurgen Bauer (a3), Rainer M. Bohle (a4), Karl J. Hagel (a3), Peter G.J. Nikkels (a5) and Friedrich W. Hehrlein (a2)...

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