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Successful implantation of a dual-chamber pacemaker in an ELBW infant for long QT syndrome

  • Brian McCrossan (a1), Yves d’Udekem (a2), Andrew Mark Davis (a1) and Andreas Pflaumer (a1)


Long QT syndromes encompass the most prevalent group of ion channelopathies. Long QT syndromes are predominantly familial and predispose the affected individual to ventricular arrhythmias and sudden death. Permanent pacemaker insertion for long QT syndrome is discouraged apart from younger patients exhibiting 2:1 atrioventricular block. However, permanent pacemaker insertion is a relatively common procedure in neonates with atrioventricular block, and dual-chamber permanent pacemaker insertion in low birth weight infants is challenging. We describe the management of long QT syndrome − type 2 − presenting in an extremely preterm neonate including epicardial, dual-chamber permanent pacemaker insertion.


Corresponding author

Correspondence to: Dr B. McCrossan, Department of Paediatric Cardiology, Royal Children’s Hospital, 50 Flemington Road, Parkville, Melbourne, Victoria 3052, Australia. Tel: +613 9345 5713; Fax: +613 9345 6001; E-mail:


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