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A rare association: first degree AV block and long QT syndrome

Published online by Cambridge University Press:  06 June 2019

Taner Kasar ,
H. Candas Kafali  and
Yakup Ergul
Taner Kasar*
Affiliation:
Pediatric Cardiology, Saglik Bilimleri University Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Research and Training Hospital, Istanbul, Turkey
H. Candas Kafali
Affiliation:
Pediatric Cardiology, Saglik Bilimleri University Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Research and Training Hospital, Istanbul, Turkey
Yakup Ergul
Affiliation:
Pediatric Cardiology, Saglik Bilimleri University Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Research and Training Hospital, Istanbul, Turkey
*
Author for correspondence: Taner Kasar, Pediatric Cardiology, Saglik Bilimleri University Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Research and Training Hospital, Istasyon Mah, Turgut Özal Bulvari No:11 Küçükçekmece, Istanbul, Turkey. Tel: +90 212 692 2000; GSM: +90 505 886 0810; Fax: +90 212 471 9494; E-mail: taner.kasar@hotmail.com
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Abstract

The coexistence of long QT syndrome with 2:1 or complete atrioventricular blocks has been reported in the literature, but, to the best of our knowledge, this is the first pediatric case of long QT syndrome coexisting with first-degree atrioventricular blocks(1–3).

Keywords

Long QT syndromefirst-degree atrioventricular blockKCNH2 mutation
Type
Images in Congenital Cardiac Disease
Information
Cardiology in the Young , Volume 29 , Issue 5 , May 2019 , pp. 697 - 698
Copyright
© Cambridge University Press 2019 

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References

Garson, A Jr, Dick, M 2nd, Fournier, A, et al. The long QT syndrome in children. An international study of 287 patients. Circulation 1993; 87: 1866–1872.CrossRefGoogle Scholar
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