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Prenatal diagnosis of isolated total anomalous systemic venous connection to the left atrium

Published online by Cambridge University Press:  08 June 2017

Béatrice Miltner
Affiliation:
The Pediatric Cardiology Unit, Department of Pediatrics, Cliniques universitaires Saint-Luc (UCL), Brussels, Belgium
Alain Jean Poncelet
Affiliation:
The Department of Cardiovascular Surgery, Cliniques universitaires Saint-Luc (UCL), Brussels, Belgium
Catherine Barrea*
Affiliation:
The Pediatric Cardiology Unit, Department of Pediatrics, Cliniques universitaires Saint-Luc (UCL), Brussels, Belgium
*
Correspondence to: C. Barrea, MD, PhD, Cardiologie pédiatrique, Cliniques universitaires Saint-Luc, Av. Hippocrate 10, B-1200 Brussels, Belgium. Tel: +32 (0)2 764 13 80; Fax: +32 (0)2 764 89 11; E-mail: catherine.barrea@uclouvain.be

Abstract

We report the prenatal diagnosis and the neonatal follow-up of a patient with isolated total abnormal systemic venous connection to the left atrium. Right-sided and left-sided superior caval veins and the inferior caval vein were all connected to the left atrium. Pulmonary venous return was normal. This was associated with some right ventricular underdevelopment. To our knowledge, this is the first fetal description of this very rare congenital cardiac malformation.

Type
Brief Report
Copyright
© Cambridge University Press 2017 

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