Hostname: page-component-848d4c4894-2xdlg Total loading time: 0 Render date: 2024-06-22T06:27:24.607Z Has data issue: false hasContentIssue false
  • English
  • Français

Persistent left superior vena cava draining into the unroofed coronary sinus in a patient with tetralogy of Fallot and coronary sinus orifice atresia

Published online by Cambridge University Press:  21 November 2022

Arif Selcuk Open the ORCID record for Arif Selcuk [Opens in a new window] ,
Oktay Korun  and
Ahmet Sasmazel
Arif Selcuk*
Affiliation:
Department of Pediatric Cardiac Surgery, Cengiz Gokcek Gynecology, Obstetrics and Children’s Hospital, Gaziantep, Turkey
Oktay Korun
Affiliation:
Department of Pediatric Cardiac Surgery, Cerrahpasa Medical Faculty Hospital, Istanbul, Turkey
Ahmet Sasmazel
Affiliation:
Department of Pediatric Cardiac Surgery, Medipol Mega Univesity Hospital, Istanbul, Turkey
*
Author for correspondence: Arif Selcuk, MD, Cengiz Gokcek Gynecology, Obstetrics and Children’s Hospital Sehitkamil, Gaziantep, 27010, Turkey. Tel: +90 342 360 0888; Fax: +90 342 360 0290. E-mail: kdcaselcuk@gmail.com
Get access Rights & Permissions [Opens in a new window]

Abstract

Introduction:

In this study, we present a case of directing persistent left superior vena cava drainage into the unroofed coronary sinus to the right atrium in a patient with tetralogy of Fallot and coronary sinus orifice atresia without innominate vein.

Case report:

A 16-month-old boy diagnosed with tetralogy of Fallot was admitted. Following intracardiac repair, the left superior vena cava was divided from the left atrial junction, passed through under the ascending aorta and anastomosed to the right superior vena cava.

Conclusion:

To our knowledge, this is the first patient reported with persistent left superior vena cava, unroofed coronary sinus, coronary sinus orifice atresia, and tetralogy of Fallot. The extracardiac direct anastomosis technique was used successfully to direct persistent left superior vena cava to the right atrium without any post-procedure complications

Keywords

Tetralogy of Fallotsurgery/techniquesvenous disease
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 7 , July 2023 , pp. 1199 - 1200
Check for updates
Copyright
© The Author(s), 2022. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Caballero, RP, Izquierdo, BP, Jaurena, JMG. Raghib syndrome. Surgical treatment. Rev Esp Cardiol 2016; 69: 71.CrossRefGoogle Scholar
Nomura, K, Kurosawa, H, Morita, K, Miyamoto, H, Tatara, A, Hanai, M. A surgical case report-rare association of tetralogy of Fallot with cor triatriatum, unroofed coronary sinus and persistent left superior vena cava. Nippon Kyobu Geka Gakkai Zasshi 1997; 45: 92–95.Google ScholarPubMed
Ueno, T, Sakata, R, Iguro, Y, et al. Radical repair of cor triatriatum with partially unroofed coronary sinus and perisitent left superior vena cava 35 years after operation for tetralogy of Fallot. J Card Surg 2008; 23: 747–749.CrossRefGoogle Scholar
Jian, Z, Li, J, Xiao, Y. Rare association of Tetralogy of Fallot with partial unroofed coronary sinus and PLSVC: case report. Thorac Cardiov Surg 2010; 58: 113–119.CrossRefGoogle Scholar
Muthialu, N, Rao, M, Balakrishnan, S. Unusual combination of unroofed coronary sinus in a setting of atrioventricular septal defect with Tetralogy of Fallot - a case report. Indian J Thorac Cardiovasc Surg 2014; 30: 152–154.CrossRefGoogle Scholar
Mallula, KK, Patel, ND, Abdulla, R, Bokowski, JW. Tetralogy of Fallot with left superior vena cava and coronary sinus atrial septal defect: a rare association. Pediatr Cardiol 2015; 36: 1100–1101.10.1007/s00246-015-1137-1CrossRefGoogle ScholarPubMed
Hahm, JK, Park, YW, Lee, JK, Choi, JY, Sul, JH, Lee, SK. Magnetic resonance imaging of unroofed coronary sinus: three cases. Pediatr Cardiol 2000; 21: 382–387.CrossRefGoogle ScholarPubMed
Xie, MX, Yang, YL, Cheng, TO, et al. Coronary sinus septal defect (unroofed coronary sinus): echocardiographic diagnosis and surgical treatment. Int J Cardiol 2013; 168: 1258–1263.CrossRefGoogle ScholarPubMed
Webb, W, Gamsu, G, Speckman, J, Kaiser, J, Federle, M, Lipton, M. Computed tomographic demonstration of mediastinal venous anomalies. Am J Roentgenol 1982; 139: 157–161.CrossRefGoogle ScholarPubMed
Van Son, JAM, Hambsch, J, Mohr, FW. Repair of complex unroofed coronary sinus by anastomosis of left to right superior vena cava. Ann Thorac Surg 1998; 65: 280–281.CrossRefGoogle ScholarPubMed