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The nomenclature, definition and classification of discordant atrioventricular connections

  • Jeffrey P. Jacobs (a1), Rodney C.G. Franklin (a2), James L. Wilkinson (a3), Andrew D. Cochrane (a4), Tom R. Karl (a5), Vera D. Aiello (a6), Marie J. Béland (a7), Steven D. Colan (a8), Martin J. Elliott (a9), J. William Gaynor (a10), Otto N. Krogmann (a11), Hiromi Kurosawa (a12), Bohdan Maruszewski (a13), Giovanni Stellin (a14), Christo I. Tchervenkov (a15) and Paul M. Weinberg (a16)...

Abstract

Congenitally corrected transposition is a complex cardiac lesion that is often associated with ventricular septal defect, obstruction of the outflow tract of the morphologically left ventricle, and abnormalities of the morphologically tricuspid valve.1,2 Nomenclature for this lesion has been variable and confusing.1 In this review, we define, and hopefully clarify this terminology. The lesion is a combination of discordant union of the atrial chambers with the ventricles, and the ventricles with the arterial trunks.1,2 In rare circumstances, discordant atrioventricular connections can be associated with concordant ventriculo-arterial connections. This malformation has been called “isolated ventricular inversion”. The term is less than precise, and the descriptive approach using the phrase “discordant atrioventricular connections with concordant ventriculo-arterial connections” is preferred, as discussed below.

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Copyright

Corresponding author

Correspondence to: Jeffrey P. Jacobs MD, FACS, FACC, FCCP, Cardiovascular and Thoracic Surgeon, The Congenital Heart Institute of Florida (CHIF), Clinical Associate Professor University of South Florida (USF), Cardiac Surgical Associates (CSA), 603 Seventh Street South, Suite 450, Saint Petersburg, FL 33701, United States of America. Tel: +727 822 6666; Fax: +727 821 5994; E-mail: JeffJacobs@msn.com

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References

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