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Long-term follow-up after staged reconstruction or transplantation for patients with functionally univentricular heart

Published online by Cambridge University Press:  21 September 2005

Gil Wernovsky  and
Maryanne R. K. Chrisant
Gil Wernovsky
Affiliation:
Division of Pediatric Cardiology, Children's Hospital of Philadelphia, Philadelphia, USA
Maryanne R. K. Chrisant
Affiliation:
Department of Pediatrics, University of Pennsylvania School of Medicine, Pennsylvania, USA
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Extract

As recently as 35 years ago, children born with a functionally single ventricle were destined to a lifetime of multiple palliative operations, and disrupted growth and development. Physical signs of their cardiac disease were evidenced by chronic hypoxemia, polycythemia, clubbing, small stature, and severely reduced exercise ability. A normal lifestyle, with typical landmarks such as uninterrupted adolescence and potential childbearing, was unlikely. The successful application of right heart bypass by Fontan and Kreutzer in the early 1970s heralded an era of multiple medical and surgical breakthroughs that have systematically improved the quality of life and long-term outlook for these children.

Type
Long-Term Follow-up and Future Implications
Information
Cardiology in the Young , Volume 14 , Issue S1 , February 2004 , pp. 115 - 126
Copyright
© 2004 Cambridge University Press

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