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Left ventricular non-compaction in a child with bicuspid aortic valve and aortic coarctation

Published online by Cambridge University Press:  05 August 2019

Ageliki Karatza ,
Konstantinos S. Mylonas Open the ORCID record for Konstantinos S. Mylonas [Opens in a new window]  and
Aphrodite Tzifa
Ageliki Karatza*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, General University Hospital of Patras, Patras, Greece
Konstantinos S. Mylonas
Affiliation:
Department of Pediatric Cardiology and Adult Congenital Heart Disease, Mitera Children’s Hospital, Athens, Greece
Aphrodite Tzifa
Affiliation:
Department of Pediatric Cardiology and Adult Congenital Heart Disease, Mitera Children’s Hospital, Athens, Greece
*
Author for correspondence: Ageliki Karatza, MD, PhD, Division of Pediatric Cardiology, Department of Pediatrics, General University Hospital of Patras, Patras, 26504; Greece. Tel: (+30) 2610999821; (+30) 6947317427; Fax: (+30) 2610994533; E-mail: agelikikaratza@hotmail.com
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Abstract

We present the case of a 3-year-old boy with bicuspid aortic valve, aortic coarctation, and left ventricular non-compaction. The diagnosis was made post-natally with ultrasonography and was verified by cardiac MRI. Aortic coarctation was initially repaired surgically. At age 3 months, recoarctation and heart failure developed. Balloon angioplasty was performed with immediate improvement. At age 3 years, the patient remains asymptomatic and normotensive.

Keywords

Left ventricular non-compactiontrabeculationsbicuspid aortic valveaortic coarctationcongenital heart disease
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 9 , September 2019 , pp. 1208 - 1210
Copyright
© Cambridge University Press 2019 

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