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Isolated right subclavian artery arising from the right pulmonary artery via a right-sided ductus arteriosus with associated pulmonary steal phenomenon

  • Stephen G. Miller (a1), Michael J. Campbell (a1), Piers C.A. Barker (a1) and Kevin D. Hill (a1)


We present a patient with DiGeorge syndrome and an isolated right subclavian artery arising from the right pulmonary artery via a right-sided ductus arteriosus. The patient showed a subclavian and pulmonary steal with perfusion of the right arm and right lung via retrograde circulation in the right vertebral artery. The patient underwent successful surgical repair.


Corresponding author

Correspondence to: Dr K. Hill, Division of Pediatric Cardiology, Department of Pediatrics, Duke University Medical Center, PO Box 3090, Durham, North Carolina 27710, United States of America. Tel: (919) 681 2880; Fax: 001919 681 8927; E-mail:


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