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Inferior sinus venosus defect and anomalous hepatic venous return to the coronary sinus leading to an Eisenmenger syndrome

Published online by Cambridge University Press:  28 April 2022

Asma Tajouri
Affiliation:
Marie-Lannelongue Hospital, Paediatric and Congenital Cardiac Surgery Department, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C Groupe Hospitalier Saint-Joseph, Paris-Saclay University, Plessis-Robinson, France
Clément Batteux
Affiliation:
Marie-Lannelongue Hospital, Paediatric and Congenital Cardiac Surgery Department, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C Groupe Hospitalier Saint-Joseph, Paris-Saclay University, Plessis-Robinson, France UMRS 999, INSERM, Marie-Lannelongue Hospital, Paris-Saclay University, Le Plessis Robinson, France
Reaksmei Ly
Affiliation:
Hôpital Européen Georges Pompidou, adult congenital Cardiology Unit, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C, Paris, France
Lucile Houyel
Affiliation:
Hôpital Necker-Enfants Malades, Congenital and Pediatric Cardiology Unit, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C, Paris, France. Université de Paris, Paris, France
Sebastien Hascoet*
Affiliation:
Marie-Lannelongue Hospital, Paediatric and Congenital Cardiac Surgery Department, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C Groupe Hospitalier Saint-Joseph, Paris-Saclay University, Plessis-Robinson, France UMRS 999, INSERM, Marie-Lannelongue Hospital, Paris-Saclay University, Le Plessis Robinson, France
*
Author for correspondence: Sebastien Hascoet, Hôpital Marie Lannelongue, 133 avenue de la résistance, 92350, Le Plessis-Robinson, France. Tel: 0033 1 40 94 28 00. E-mail: s.hascoet@ghpsj.fr

Abstract

Inferior sinus venosus defect associated with left hepatic vein drainage to the coronary sinus is an extremely rare condition. We report the case of a 41-year-old man suffering from pulmonary arterial hypertension related to this unusual CHD. Planning of heart–lung transplantation in this case required accurate anatomical description.

Type
Brief Report
Copyright
© The Author(s), 2022. Published by Cambridge University Press

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References

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