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Hypoplastic left heart in Turner’s syndrome: a primary indication for transplant?

Part of: Hypoplastic Left Heart Syndrome (HLHS)

Published online by Cambridge University Press:  13 December 2017

Joseph Philip ,
Dipankar Gupta ,
Mark S. Bleiweis ,
Biagio A. Pietra  and
Himesh V. Vyas
Joseph Philip*
Affiliation:
Congenital Heart Center, UF Health Shands Children’s Hospital, University of Florida, Gainesville, Florida, United States of America
Dipankar Gupta
Affiliation:
Congenital Heart Center, UF Health Shands Children’s Hospital, University of Florida, Gainesville, Florida, United States of America
Mark S. Bleiweis
Affiliation:
Congenital Heart Center, UF Health Shands Children’s Hospital, University of Florida, Gainesville, Florida, United States of America
Biagio A. Pietra
Affiliation:
Congenital Heart Center, UF Health Shands Children’s Hospital, University of Florida, Gainesville, Florida, United States of America
Himesh V. Vyas
Affiliation:
Congenital Heart Center, UF Health Shands Children’s Hospital, University of Florida, Gainesville, Florida, United States of America
*
Correspondence to: J. Philip, MD, Congenital Heart Center, UF Health Shands Children’s Hospital, University of Florida, 1600 SW Archer road, PO Box 100297 Gainesville, FL 32610, United States of America. Tel: +1 352 273 7770; Fax: +352 273 5927; E-mail: subijo9@ufl.edu
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Abstract

Survival for hypoplastic left heart syndrome patients following the Norwood procedure is 71–90%. Mortality in patients with Turner’s syndrome and hypoplastic left heart syndrome after conventional palliation (Norwood operation) has been reported as high as 80%. This questions the approach of traditional staged palliation. Here, we report a patient with hypoplastic left heart syndrome and Turner’s syndrome bridged to orthotopic heart transplantation following a hybrid procedure.

Keywords

Turner’s syndromehybrid palliationheart transplanthypoplastic left heart syndrome
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 3 , March 2018 , pp. 458 - 460
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Copyright
© Cambridge University Press 2017 

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References

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