Hostname: page-component-77c89778f8-9q27g Total loading time: 0 Render date: 2024-07-17T17:56:01.028Z Has data issue: false hasContentIssue false
  • English
  • Français

Haemodynamic consequences following closure of an Abernethy malformation in a patient following a total cavopulmonary shunt

Published online by Cambridge University Press:  21 February 2018

Deepa Sasikumar ,
Bijulal Sasidharan  and
Anoop Ayyappan
Deepa Sasikumar
Affiliation:
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
Bijulal Sasidharan*
Affiliation:
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
Anoop Ayyappan
Affiliation:
Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
*
Author for correspondence: Bijulal Sasidharan, Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, 695011, India. Tel: +91 94465 90185; Fax: 91 471 2446433; E-mail: drbijulalsasidharan@gmail.com
Get access Rights & Permissions [Opens in a new window]

Abstract

A 17-year-old girl with situs ambiguous, hypoplastic right ventricle with a large ventricular septal defect, and severe pulmonary stenosis had undergone Kawashima operation 10 years back. She had significant desaturation because of a large Abernethy malformation, with reverse shunting from the inferior caval vein to the portal vein. It was closed with a vascular plug, with improvement in oxygen saturation. She developed extensive inferior caval vein thrombus following the procedure, which was managed conservatively by anti-coagulation.

Keywords

AbernethyheterotaxyKawashima
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 5 , May 2018 , pp. 768 - 770
Copyright
© Cambridge University Press 2018 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Morgan, G, Superina, R. Congenital absence of the portal vein: two cases and a proposed classification system for portasystemic vascular anomalies. J Pediatr Surg 1999; 29: 1239–1241.Google Scholar
2. Kothari, SS. Non-cardiac issues in patients with heterotaxy syndrome. Ann Pediatr Cardiol 2014; 7: 187–192.Google Scholar
3. Ratnasamy, C, Kubegov, A, Swaminathan, S. Cardiac anomalies in the setting of the Abernethy malformation of the portal vein. Cardiol Young 2007; 17: 212–214.CrossRefGoogle ScholarPubMed
4. Doraiswamy, V, Sivakumar, K. Impact of Abernathy malformation on pulmonary circulatory hemodynamics in a univentricular heart. Ann Pediatr Cardiol 2017; 10: 90–91.Google Scholar
5. Knirsch, W, Benz, DC, Bühr, P, et al. Catheter interventional treatment of congenital portosystemic venous shunts in childhood. Catheter Cardiovasc Interv. 2016; 87: 1281–1292.Google Scholar

Sasikumar et al. supplementary material 1

Supplementary Video

Download Sasikumar et al. supplementary material 1(Video)
Video 9.1 MB

Sasikumar et al. supplementary material 2

Supplementary Video

Download Sasikumar et al. supplementary material 2(Video)
Video 7.7 MB

Sasikumar et al. supplementary material 3

Supplementary Video

Download Sasikumar et al. supplementary material 3(Video)
Video 2.8 MB