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Generalised lymphangiomatosis in an 8-year-old girl who presented with cardiomegaly

Published online by Cambridge University Press:  02 March 2011

Funda Öztunç ,
Bülent Koca  and
İbrahim Adaletli
Funda Öztunç
Affiliation:
Department of Pediatric Cardiology, Istanbul University, Istanbul, Turkey
Bülent Koca*
Affiliation:
Department of Pediatric Cardiology, Istanbul University, Istanbul, Turkey
İbrahim Adaletli
Affiliation:
Cerrahpaşa Medical Faculty, Department of Radiology, Istanbul University, Istanbul, Turkey
*
Correspondence to: Dr B. Koca, MD, İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Çocuk Kardiyoloji Bilim Dalı, İstanbul, Turkey. Tel: +90 212 4143000; Fax: +90 (212) 6328633; E-mail: bkoca78@yahoo.com
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Abstract

Generalised lymphangiomatosis is a rare disease that is characterized by widespread bony and soft tissue involvement of lymphangioma. Radiological evaluation is crucial because the site and extent of the lymphangioma are important prognostic factors. The computed tomography, ultrasonography and magnetic resonance images showed sharply defined, non-enhanced cystic lesions involving the mediastinum, bones, spleen, lung, and lower neck. We report here a case that was referred to us for investigation of marked cardiomegaly.

Keywords

Mediastinal tumourscystic massechocardiographymagnetic resonance imaging
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 4 , 12 July 2011 , pp. 465 - 467
Copyright
Copyright © Cambridge University Press 2011

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