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Fistula between the right pulmonary artery and the left atrium—an unusual cause of cyanotic heart disease

  • Kjell Saatvedt (a1), Gunnar Stake (a2) and Harald Lindberg (a1)

Abstract

A fistula from the pulmonary artery to the left atrium is a very rare congenital anomaly. The communication, almost exclusively arising from the right pulmonary artery, may give rise to a variety of symptoms with cyanosis as the predominant sign. To our knowledge only seven neonates have been reported with this anomaly, and five of them died postoperatively. We present another two neonates with such a fistula which was closed by simple ligation using a transsternal approach and cardiopulmonary bypass. Both patients had an uneventful postoperative course and are alive and well at the age of two and three years, respectively.

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Corresponding author

Dr. Kjell Saatvedt, Surgical Department A, Cardiothoracic Unit, Rikshospitalet, 0027 Oslo, Norway. Tel. 228670 10; Fax. 228672 63.

References

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Keywords

Fistula between the right pulmonary artery and the left atrium—an unusual cause of cyanotic heart disease

  • Kjell Saatvedt (a1), Gunnar Stake (a2) and Harald Lindberg (a1)

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