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Double outlet right atrium with coexisting double inlet left ventricle and concordant ventriculoarterial connections: a fascinating variant of the Holmes heart

Published online by Cambridge University Press:  23 July 2010

Louise Coats*
Affiliation:
Department of Cardiology, Wansbeck Hospital, Northumberland, United Kingdom
Craig Runnett
Affiliation:
Department of Cardiology, Wansbeck Hospital, Northumberland, United Kingdom
Duwarakan K. Satchithananda
Affiliation:
Department of Cardiology, Wansbeck Hospital, Northumberland, United Kingdom
*
Correspondence to: Dr L. Coats, Department of Cardiology, Wansbeck Hospital, Woodhorn Lane, Ashington NE63 9JJ, Northumberland. Tel: 0844 811 8111; Fax: 0167 052 9414; E-mail: lecoats@doctors.org.uk

Abstract

Occasionally complex congenital cardiac disease presents for the first time in adulthood, encouraging us to reflect anew on our understanding of familiar conditions. A 59-year–old woman, who had had two normal pregnancies, attended with breathlessness and was found to have a double inlet left ventricle with concordant ventriculoarterial connections and a straddling tricuspid valve adherent to the malaligned ventricular septum.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 2010

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