Hostname: page-component-848d4c4894-8kt4b Total loading time: 0 Render date: 2024-06-22T22:40:01.803Z Has data issue: false hasContentIssue false
  • English
  • Français

Complete tracheal rings and hypoplastic left heart variant: a rare and fatal association

Part of: Cardiac Morphology

Published online by Cambridge University Press:  24 January 2019

Neha Bansal Open the ORCID record for Neha Bansal [Opens in a new window] ,
Deemah R. Mahadin  and
Sanjeev Aggarwal
Neha Bansal*
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Deemah R. Mahadin
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Sanjeev Aggarwal
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
*
Author for correspondence: N. Bansal, MD, Division of Cardiology, Children’s Hospital of Michigan, 3901 Beaubien Blvd, Detroit, MI 48201, USA. Tel: +1(313) 745-5481; Fax: +1 313 939 0894; E-mail: nehban@gmail.com
Get access Rights & Permissions [Opens in a new window]

Abstract

Congenital complete tracheal rings are usually associated with pulmonary slings. We report a rare association of congenital complete tracheal rings with hypoplastic left heart variant. A term infant with diagnosis of a mildly hypoplastic mitral valve, unicuspid aortic valve, and moderately hypoplastic aortic arch with severe coarctation underwent a hybrid procedure initially. Upon failing extubation attempts, complete tracheal rings were seen on direct laryngoscopy. The combination of the lesions resulted in a poor outcome. In patients with failure of extubation post-cardiac surgery, a diagnosis of complete tracheal rings should be included in the differential and a direct laryngoscopy should be considered.

Keywords

Complete tracheal ringshypoplastic left heartunicuspid aortic valve
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 3 , March 2019 , pp. 445 - 447
Copyright
© Cambridge University Press 2019 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Footnotes

Cite this article: Bansal N, Mahadin DR, Aggarwal S. (2019) Complete tracheal rings and hypoplastic left heart variant: a rare and fatal association. Cardiology in the Young29: 445–447. doi: 10.1017/S1047951118002391

References

1. Tsai, MH, Wong, KS, Lien, R, Huang, HR, Liao, SL, Hsu, JF. Heliox as the rescue therapy for a neonate with congenital tracheal stenosis, pulmonary artery sling, and intracardiac anomalies. Am J Perinatol 2009; 26 (5): 357–360.Google Scholar
2. Chao, YC, Peng, CC, Lee, KS, Lin, SM, Chen, MR. The association of congenital tracheobronchial stenosis and cardiovascular anomalies. Int J Pediatr Otorhinolaryngol 2016; 83: 1–6.Google Scholar
3. Butler, CR, Speggiorin, S, Rijnberg, FM, et al. Outcomes of slide tracheoplasty in 101 children: a 17-year single-center experience. J Thorac Cardiovasc Surg 2014; 147 (6): 1783–1789.Google Scholar
4. Loukanov, T, Sebening, C, Springer, W, Ulmer, H, Hagl, S. Simultaneous management of congenital tracheal stenosis and cardiac anomalies in infants. J Thorac Cardiovasc Surg 2005; 130 (6): 1537–1541.Google Scholar
5. Rossi, ME, Moreddu, E, Mace, L, Triglia, JM, Nicollas, R. Surgical management of children presenting with surgical-needed tracheal stenosis. Int J Pediatr Otorhinolaryngol 2018; 108: 219–223.Google Scholar
6. Hofferberth, SC, Watters, K, Rahbar, R, Fynn-Thompson, F. Management of congenital tracheal stenosis. Pediatrics 2015; 136 (3): e660–e669.Google Scholar
7. McLaughlin, FJ, Strieder, DJ, Harris, GB, Vawter, GP, Eraklis, AJ. Tracheal bronchus: association with respiratory morbidity in childhood. J Pediatr 1985; 106 (5): 751–755.10.1016/S0022-3476(85)80348-6Google Scholar
8. Anton-Pacheco, JL, Cano, I, Garcia, A, Martinez, A, Cuadros, J, Berchi, FJ. Patterns of management of congenital tracheal stenosis. J Pediatr Surg 2003; 38 (10): 1452–1458.Google Scholar