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Clues to echocardiographic diagnosis of isolation of right subclavian artery in a patient with DiGeorge syndrome and its transcatheter management with its associated anomalies

Published online by Cambridge University Press:  10 September 2019

Asish R. Mohakud
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
Sreeja Pavithran
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
Kothandam Sivakumar*
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
*
Address for correspondence: Dr K. Sivakumar, MD, DM, Department of Pediatric Cardiology, Institute of Cardiovascular Diseases, Madras Medical Mission, 4A, Dr J J Nagar, Mogappair, Chennai 600089, India. Tel: +91 9444449966; Fax: +91 44 26565859; E-mail: drkumarsiva@hotmail.com

Abstract

Isolated subclavian artery is a rare anomaly. A second steal due to a patent arterial duct further reduces arm perfusion. Surgical anastomosis of the isolated vessel to aorta normalises arm perfusion. Simple echocardiographic clues aid in the diagnosis. An associated moderate sized ventricular septal defect was non-surgically closed along with catheter closure of the duct resulting in improved arm perfusion.

Type
Brief Report
Copyright
© Cambridge University Press 2019 

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