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Cardiac anomalies in the setting of the Abernethy malformation of the portal vein

  • Christopher Ratnasamy (a1), Amethyst Kurbegov (a2) and Sethuraman Swaminathan (a1)

Abstract

We describe a child with tricuspid atresia associated with a porto-systemic shunt and complete absence of the portal vein, the latter known as the Abernethy malformation. As far as we are aware, this association has not previously been reported. We review the various cardiac defects that have been reported in children with the Abernethy malformation, emphasizing the interesting clinical presentations of this rare malformation of the portal venous system.

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Corresponding author

Correspondence to: Sethuraman Swaminathan, Division of Pediatric Cardiology, P.O. Box 016960 (R-76), Miami, FL 33101, United States of America. Tel: +305 585 6683; Fax: +305 324 6012; E-mail: sswami@med.miami.edu

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References

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Keywords

Cardiac anomalies in the setting of the Abernethy malformation of the portal vein

  • Christopher Ratnasamy (a1), Amethyst Kurbegov (a2) and Sethuraman Swaminathan (a1)

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