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Atypical atrioventricular nodal reentry tachycardia in a child with polyvalvular dysplasia

Published online by Cambridge University Press:  09 May 2014

Jonathan N. Johnson*
Affiliation:
Department of Pediatrics/Division of Pediatric Cardiology, Mayo Clinic, Rochester, Minnesota, United States of America
Michael J. Ackerman
Affiliation:
Department of Pediatrics/Division of Pediatric Cardiology, Mayo Clinic, Rochester, Minnesota, United States of America Department of Molecular Pharmacology and Experimental Therapeutics, Mayo Clinic, Rochester, Minnesota, United States of America Department of Medicine/Division of Cardiovascular Diseases, Mayo Clinic, Rochester, Minnesota, United States of America
Bryan C. Cannon
Affiliation:
Department of Pediatrics/Division of Pediatric Cardiology, Mayo Clinic, Rochester, Minnesota, United States of America
*
Correspondence to: J. N. Johnson, MD, Pediatric Cardiology, Mayo Clinic, Gonda 6-138SW, 200 First Street SW, Rochester, MN 55905, United States of America. Tel: +507 266 0676; Fax: +507 284 3968; E-mail: johnson.jonathan@mayo.edu

Abstract

A 10-year-old boy with polyvalvular dysplasia and severe involvement of both atrioventricular valves presented with palpitations. Concern was raised for atrial tachyarrhythmia due to biatrial enlargement; however, ambulatory monitoring discovered a reentrant mechanism. Electrophysiology study revealed atypical atrioventricular nodal reentrant tachycardia involving two components of the slow pathway, with inputs in the posterior septum around his dysplastic tricuspid valve. He underwent successful modification of the slow pathway using cryoablation.

Type
Brief Reports
Copyright
© Cambridge University Press 2014 

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