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Atrioventricular valve surgery in patients with univentricular heart and two separate atrioventricular valves

Published online by Cambridge University Press:  03 April 2024

Benedikt Mayr*
Affiliation:
Department of Cardiovascular Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Department of Cardiovascular Surgery, Insure (Institute for Translational Cardiac Surgery), German Heart Centre Munich at the Technical University of Munich, Munich, Germany
Takuya Osawa
Affiliation:
Department of Congenital and Pediatric Heart Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Division of Congenital and Pediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-University, Munich, Germany
Helena Staehler
Affiliation:
Department of Congenital and Pediatric Heart Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Division of Congenital and Pediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-University, Munich, Germany
Thibault Schaeffer
Affiliation:
Department of Congenital and Pediatric Heart Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Division of Congenital and Pediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-University, Munich, Germany
Christoph Röhlig
Affiliation:
Department of Pediatric Cardiology and Congenital Heart Disease, German Heart Centre Munich at the Technical University Munich, Munich, Germany
Julie Cleuziou
Affiliation:
Department of Congenital and Pediatric Heart Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Division of Congenital and Pediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-University, Munich, Germany
Alfred Hager
Affiliation:
Department of Pediatric Cardiology and Congenital Heart Disease, German Heart Centre Munich at the Technical University Munich, Munich, Germany
Peter Ewert
Affiliation:
Department of Pediatric Cardiology and Congenital Heart Disease, German Heart Centre Munich at the Technical University Munich, Munich, Germany
Jürgen Hörer
Affiliation:
Department of Congenital and Pediatric Heart Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Division of Congenital and Pediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-University, Munich, Germany
Rüdiger Lange
Affiliation:
Department of Cardiovascular Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Department of Cardiovascular Surgery, Insure (Institute for Translational Cardiac Surgery), German Heart Centre Munich at the Technical University of Munich, Munich, Germany DZHK (German Center for Cardiovascular Research)-partner Site Munich Heart Alliance, Munich, Germany
Masamichi Ono
Affiliation:
Department of Congenital and Pediatric Heart Surgery, German Heart Centre Munich at the Technical University Munich, Munich, Germany Division of Congenital and Pediatric Heart Surgery, University Hospital of Munich, Ludwig-Maximilians-University, Munich, Germany
*
Corresponding author: Benedikt Mayr; Email: mayrb@dhm.mhn.de

Abstract

Objectives:

Atrioventricular valve regurgitation in patients with univentricular heart is a well-known risk factor for adverse outcomes and atrioventricular valve repair remains a particular surgical challenge.

Methods:

We reviewed all surgical atrioventricular valve procedures in patients with univentricular heart and two separate atrioventricular valves who underwent surgical palliation. Endpoints of the study were reoperation-free survival and cumulative incidence of reoperation.

Results:

Between 1994 and 2021, 202 patients with univentricular heart and two separate atrioventricular valve morphology underwent surgical palliation, with 15.8% (32/202) requiring atrioventricular valve surgery. Primary diagnoses were double inlet left ventricle (n = 14, 43.8%), double outlet right ventricle (n = 7, 21.9%), and congenitally corrected transposition of the great arteries (n = 7, 21.9%). Median weight at valve surgery was 10.6 kg (interquartile range, 7.9–18.9). Isolated left or right atrioventricular valve surgery was required in nine (28.1%) and 22 patients (68.8%), respectively. Concomitant left and right atrioventricular valve surgery was performed in one patient (3.1%). Closure of the left valve was conducted in four patients (12.5%) and closure of the right valve in three (9.4%). Operative and late mortality were 3.1% and 9.7%, respectively. Reoperation-free survival and cumulative incidence of reoperation at 10 years after surgery were 62.3% (standard error of the mean: 6.9) and 30.9% (standard error of the mean: 9.6), respectively.

Conclusions:

In patients with univentricular heart and two separate atrioventricular valves, surgical intervention on these valves is required in a minority of patients and is associated with low mortality but high incidence of reoperation.

Type
Original Article
Copyright
© The Author(s), 2024. Published by Cambridge University Press

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