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Aortic root aneurysm repair in a neonate with Loeys–Dietz syndrome

Part of: Surgery

Published online by Cambridge University Press:  25 January 2021

Willa Li Open the ORCID record for Willa Li [Opens in a new window] ,
William Cohen ,
Pamela Combs ,
Joshua Wong Open the ORCID record for Joshua Wong [Opens in a new window] ,
Rohit Loomba ,
Brian K. Lee ,
Chawki El-Zein ,
Michel Ilbawi ,
Luca Vricella  and
Narutoshi Hibino
Willa Li
Affiliation:
Section of Cardiac Surgery, Department of Surgery, The University of Chicago, Chicago, IL, USA
William Cohen
Affiliation:
Section of Cardiac Surgery, Department of Surgery, The University of Chicago, Chicago, IL, USA
Pamela Combs
Affiliation:
Section of Cardiac Surgery, Department of Surgery, The University of Chicago, Chicago, IL, USA
Joshua Wong
Affiliation:
Pediatric Cardiology, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
Rohit Loomba
Affiliation:
Pediatric Cardiology, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
Brian K. Lee
Affiliation:
Pediatric Cardiology, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
Chawki El-Zein
Affiliation:
Pediatric Cardiac Surgery, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
Michel Ilbawi
Affiliation:
Pediatric Cardiac Surgery, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
Luca Vricella
Affiliation:
Section of Cardiac Surgery, Department of Surgery, The University of Chicago, Chicago, IL, USA Pediatric Cardiac Surgery, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
Narutoshi Hibino*
Affiliation:
Section of Cardiac Surgery, Department of Surgery, The University of Chicago, Chicago, IL, USA Pediatric Cardiac Surgery, Advocate Children’s Heart Institute, Advocate Children’s Hospital, Oak Lawn, IL, USA
*
Author for correspondence: Dr N. Hibino, MD, PhD, Section of Cardiac Surgery, Department of Surgery, The University of Chicago, 5841 S. Maryland, Rm E-500, MC5040, Chicago, IL60637, USA. Tel: 773-834-3707; Fax: 773-702-4187. E-mail: nhibino@surgery.bsd.uchicago.edu
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Abstract

Loeys–Dietz syndrome is a connective tissue disorder known to cause aggressive aortopathy in paediatric patients, but it is extremely rare for cardiovascular events to present during infancy. We report the first successful aortic repair in a neonate with LDS presenting in extremis with an early onset, massive aortic aneurysm.

Keywords

Loeys–Dietz syndromeneonateaortic root aneurysm
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 5 , May 2021 , pp. 848 - 850
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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