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Anomalous origin of the right pulmonary artery from the ascending aorta accompanied by absent pulmonary valve syndrome and right-sided aortic arch: a rare case in adult congenital heart disease

Published online by Cambridge University Press:  01 July 2014

Zahra Khajali
Affiliation:
Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
Ali Mohammadzadeh
Affiliation:
Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
Marzieh Khayatzadeh*
Affiliation:
Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
*
Correspondence to: Dr M. Khayatzadeh, MD; Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran 1996911151, IR Iran. Tel: +989123276710; Fax: +982122055594; E-mail: marzi_khayat@yahoo.com

Abstract

We present a rare congenital heart disease in a 20-year-old man with anomalous origin of the right pulmonary artery from the ascending aorta, accompanied by absent pulmonary valve syndrome, and a right-sided aortic arch suspected initially in transthoracic echocardiography and subsequently confirmed by cardiac catheterisation and computed tomography angiography.

Type
Brief Reports
Copyright
© Cambridge University Press 2014 

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References

1. Fraentzel, O. Ein Fall von abnormer Communication der aorta mit der Arteria pulmonalis. Virchows Arch Pathol Ana 1868; 43: 420426.CrossRefGoogle Scholar
2. Erdem, A, Aydemir, NA, Demir, H, et al. Anomalous origin of one pulmonary artery branch from the ascending aorta: experience of our center. Arch Turk Soc Cardiol 2010; 38: 411415.Google ScholarPubMed
3. Aly, AM, Red, DA, Jiwani, A, Desai, PH. Absent pulmonary valve syndrome with left hemitruncus. AJP Rep 2012; 2: 5154.Google ScholarPubMed
4. Patel, RJ, Zakir, RM, Sethi, V, et al. Unrepaired tetralogy of Fallot with right hemitruncus in an adult: a rare case. Tex Heart Inst J 2007; 34: 250251.Google Scholar
5. Dwived, SK, Vijay, SK, Chandra, S, Saran, RK. Left hemitruncus with tetralogy of Fallot and right aortic arch: rare survival beyond the first decade. Pediatric Cardol 2012; 33: 863865.CrossRefGoogle Scholar
6. Presbitero, P, Pedretti, E, Orzan, F, et al. Absent pulmonary valve syndrome with associated anomalies of the pulmonary blood supply. Int J Cardiol 1984; 6: 587598.CrossRefGoogle ScholarPubMed