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Aerosolised heparin in the treatment of Fontan-related plastic bronchitis

  • Daniel E. Eason (a1), Kristin Cox (a2) and William B. Moskowitz (a3)


Patients with Fontan palliation and single-ventricle physiology encounter multiple comorbidities including plastic bronchitis, a disease characterised by the plugging of small and large airways by rubbery, white casts. To date, no controlled clinical trials have demonstrated effective treatment of plastic bronchitis. We report the application of aerosolised heparin, which has published success in non-cardiac-related pulmonary disease, for this complication in a Fontan patient.


Corresponding author

Correspondence to: Dr D. E. Eason, DO, MPH, Division of Pediatric Cardiology, Miller School of Medicine, University of Miami, PO Box 016960 (R-76), Miami, FL 33101, United States of America. Tel: +1 919 210 2184; Fax: +1 866 823 6013; E-mail:


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Aerosolised heparin in the treatment of Fontan-related plastic bronchitis

  • Daniel E. Eason (a1), Kristin Cox (a2) and William B. Moskowitz (a3)


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