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Unguarded mitral orifice associated with hypoplastic left heart syndrome

Published online by Cambridge University Press:  24 July 2014

Jennifer A. Su ,
John Ho  and
Pierre C. Wong
Jennifer A. Su*
Affiliation:
Division of Cardiology, Children’s Hospital Los Angeles, California, United States of America Department of Pediatrics, Keck School of Medicine, University of Southern California, Los Angeles, California, United States of America
John Ho
Affiliation:
Division of Cardiology, Children’s Hospital Los Angeles, California, United States of America Department of Pediatrics, Keck School of Medicine, University of Southern California, Los Angeles, California, United States of America
Pierre C. Wong
Affiliation:
Division of Cardiology, Children’s Hospital Los Angeles, California, United States of America Department of Pediatrics, Keck School of Medicine, University of Southern California, Los Angeles, California, United States of America
*
Correspondence to: J. A. Su, MD, Division of Cardiology, Children’s Hospital Los Angeles, 4650 W. Sunset Boulevard, Mailstop #34 Los Angeles, CA 90027, United States of America. Tel: 323 361 8308; Fax: 323 361 1513; E-mail: jsu@chla.usc.edu
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Abstract

In the spectrum of mitral valve anomalies, unguarded mitral orifice is an exceedingly rare malformation, with only four cases described in the current literature. All previously reported cases have been associated with discordant atrioventricular connections. We describe the first known case of unguarded mitral valve orifice, in the setting of atrioventricular concordance, in a newborn with hypoplastic left heart syndrome.

Keywords

Unguarded mitral orificehypoplastic left heart syndromeCHD
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Supplement 5 , June 2015 , pp. 1002 - 1005
Copyright
© Cambridge University Press 2014 

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