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Hemiazygos vein “steal hypoxic-syndrome” after hemi-Fontan operation: comprehensive four-dimensional flow magnetic resonance visualisation

Published online by Cambridge University Press:  08 March 2012

Israel Valverde*
Affiliation:
Division of Imaging Sciences and Biomedical Engineering, King's College London, The National Institute for Health Research Biomedical Research Centre at Guy's & St Thomas’ NHS Foundation Trust Department of Congenital Heart Diseases, Evelina Children's Hospital, Guy's & St Thomas’ NHS Foundation Trust, Westminster Bridge Road, London, United Kingdom
Aarthi Razishankar
Affiliation:
Division of Imaging Sciences and Biomedical Engineering, King's College London, The National Institute for Health Research Biomedical Research Centre at Guy's & St Thomas’ NHS Foundation Trust
Owen Miller
Affiliation:
Division of Imaging Sciences and Biomedical Engineering, King's College London, The National Institute for Health Research Biomedical Research Centre at Guy's & St Thomas’ NHS Foundation Trust Department of Congenital Heart Diseases, Evelina Children's Hospital, Guy's & St Thomas’ NHS Foundation Trust, Westminster Bridge Road, London, United Kingdom
Reza Razavi
Affiliation:
Division of Imaging Sciences and Biomedical Engineering, King's College London, The National Institute for Health Research Biomedical Research Centre at Guy's & St Thomas’ NHS Foundation Trust Department of Congenital Heart Diseases, Evelina Children's Hospital, Guy's & St Thomas’ NHS Foundation Trust, Westminster Bridge Road, London, United Kingdom
*
Correspondence to: Dr I. Valverde, MD, Clinical Research Assistant in Paediatric Cardiology, Division of Imaging Sciences and Biomedical Engineering, King's College London, The Rayne Institute, 4th floor, Lambeth Wing, St Thomas Hospital, London SE1 7EH, United Kingdom. Mobile: +44 (0) 7702328911; Tel: +44 (0) 2071888385; Fax: +44 (0) 2071885442; E-mail: isra.valverde@kcl.ac.uk

Abstract

A 2-year-old boy with hypoplastic left heart syndrome and previous hemi-Fontan palliation surgery was referred for cardiovascular magnetic resonance evaluation because of progressive cyanosis. This case report illustrates the advantages of non-invasive four-dimensional magnetic resonance imaging for comprehensive identification and quantification of venovenous collaterals in patients with palliated hemi-Fontan staged surgery.

Type
Brief Report
Copyright
Copyright © Cambridge University Press 2012

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References

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