Hostname: page-component-76fb5796d-skm99 Total loading time: 0 Render date: 2024-04-26T10:48:56.062Z Has data issue: false hasContentIssue false
  • English
  • Français

Moebius' syndrome: a report of two cases

Published online by Cambridge University Press:  29 June 2007

Mousa N. Jamal ,
Nabil S. Samara  and
Mohammed T. A. Al-Lozi
Mousa N. Jamal*
Affiliation:
From the Department of Otolaryngology, Faculty of Medicine, University of Jordan, Amman, Jordan.
Nabil S. Samara
Affiliation:
From the Department of Internal Medicine, Faculty of Madicine, University of Jordan, Amman, Jordan.
Mohammed T. A. Al-Lozi
Affiliation:
From the Department of Internal Medicine, Faculty of Madicine, University of Jordan, Amman, Jordan.
*
Mousa N. Jamal, M.D., Assistant Professor, Department of Otolaryngology, Jordan University Hospital, P.O. Box 13046. Amman, Jordan.
Get access Rights & Permissions [Opens in a new window]

Abstract

Two patients with Moebius' syndrome are described, a brother and a sister. In addition to bilateral congenital facial nerve paralysis, both had deafness, an external deformity of the auricles, and a latent squint. The deafness in both cases was sensorineural in type; although there was paralysis of the motor part of the facial nerve, taste and lacrimation were intact. This report shows that not all components of the facial nerve are always effected in this syndrome.

Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 102 , Issue 4 , April 1988 , pp. 350 - 352
Copyright
Copyright © JLO (1984) Limited 1988

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

El Sahy, N. (1973) Moebius syndrome associated with the mother taking thalidomide during gestation. Plastic and Reconstruction Surgery 51: 93.CrossRefGoogle Scholar
Hanson, P. A. and Rowland, L. P. (1971) Mobius syndrome and facioscapulohumeral muscular dystrophy. Archives of Neurology, 24: 31–39.Google Scholar
Henderson, J. L. (1939) The congenital facial diplegia syndrome: Clinical features, pathology and etiology. Brain, 62: 381–405.Google Scholar
Kahane, J. C. (1979) Pathophysicological effects of Moebius syndrome on speech and hearing. Archives of Otolaryngology, 105: 29–34.Google Scholar
Moebius, P. J. (1888) Ueber engeborene doppelseitige Abducens—Facialis—Laehmung. Münchener medizinische Wochenschrift 35: 9, 108.Google Scholar
Olsen, W., Wayne, B. C., Walsh, G. O. and Engel, W. K. (1970) Moebius syndrome. Lower motor neuron involvement and hypogonadism. Neurology, 20: 1002–1008.CrossRefGoogle Scholar
Rogers, B. (1971) In Plastic surgery in infancy and childhood (Mustards, , ed), pp. 348–355, W. B. Saunders Company, Philadelphia.Google Scholar
Rubinstein, A. E., Lovelace, R. E., Behrens, M. M. and Meisberg, L. A. (1975) Moebius syndrome in Kallmann's syndrome. Archives of Neurology, 32: 480–481.CrossRefGoogle Scholar
Towflghi, J., Marks, K., Palmer, E. and Vannucci, R. (1979) Moebius syndrome manopathological observation. Acta Neuropathology (Berlin), 48: 11–17.Google Scholar
Ziter, F. A., Wiser, W. C. and Rotinson, A. (1977) Three generation pedigree of Moebius syndrome variant with chromosome translocation. Archives of Neurology, 34: 437–4421.CrossRefGoogle ScholarPubMed