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Jugular foramen meningocoele in a patient with neurofibromatosis type 1

Published online by Cambridge University Press:  16 April 2007

A Siddiqui ,
S Connor  and
M Gleeson
A Siddiqui*
Affiliation:
Department of Neuroradiology, Kings College Hospital, London, UK
S Connor
Affiliation:
Department of Neuroradiology, Kings College Hospital, London, UK
M Gleeson
Affiliation:
Department of Otolaryngology, Guys Hospital, London, UK
*
Address for correspondence: A Siddiqui, Department of Neuroradiology, Ruskin wing, Kings College Hospital, Denmark Hill, London, SE5 9RS, UK. Fax: 44 (0)2032993120 E-mail: dratasiddiqui@yahoo.com
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Abstract

Objective:

We present a rare case of a jugular foramen meningocoele in a 48-year-old female, with neurofibromatosis type 1, presenting with positional vertigo. We also postulate possible underlying pathophysiological mechanisms.

Method:

We describe the imaging findings of this rare entity and review the literature on skull base meningocoeles, particularly in the context of neurofibromatosis type 1.

Results:

A computed tomography scan revealed smooth expansion of the jugular foramen. Magnetic resonance imaging showed a fluid filled lesion expanding the jugular foramen and communicating with cerebrospinal fluid of the cerebellomedullary cistern superiorly.

Conclusion:

Skull base meningocoeles are a rare entity and we believe that this is the first reported case of a meningocoele causing enlargement of the jugular foramen in a patient with neurofibromatosis type 1. The meningocoele may have resulted from a severe form of dural ectasia or from dysplastic, weakened bone at the skull base.

Keywords

MeningoceleSkull BaseNeurofibromatosis Type 1Jugular ForamenMagnetic Resonance Imaging
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 122 , Issue 2 , February 2008 , pp. 213 - 216
Copyright
Copyright © JLO (1984) Limited 2007

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