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Cochlear implantation in children with Mondini dysplasia: our experience

Published online by Cambridge University Press:  11 February 2021

N M Suri ,
A R Prasad ,
R K Sayani ,
A Anand  and
G Jaychandran
N M Suri*
Affiliation:
Department of Otorhinolaryngology, Gujarat Medical Education and Research Society (‘GMERS’) Medical College and Hospital, Gandhinagar, India
A R Prasad
Affiliation:
Department of Otorhinolaryngology, Gujarat Medical Education and Research Society (‘GMERS’) Medical College and Hospital, Gandhinagar, India
R K Sayani
Affiliation:
Department of Otorhinolaryngology, Gujarat Medical Education and Research Society (‘GMERS’) Medical College and Hospital, Gandhinagar, India
A Anand
Affiliation:
Asian Speech and Hearing Clinic, Ahmedabad, India
G Jaychandran
Affiliation:
Asian Speech and Hearing Clinic, Ahmedabad, India
*
Author for correspondence: Dr Neeraj M Suri, Department of Otorhinolaryngology, 2nd Floor, OPD Building, GMERS Medical College and Civil Hospital, Sect. 12b, near Pathikashram, Gandhinagar, Gujarat382016, India E-mail: drneerajsuri@outlook.com
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Abstract

Objective

This study details the intra-operative complications, and compares auditory scales post-implantation of either profoundly deaf young children with radiologically normal inner ears (group A) or children with Mondini dysplasia (group B).

Methods

A retrospective survey was carried out of 338 patients with severe to profound sensorineural hearing loss who underwent cochlear implant surgery from February 2015 to May 2017. Patients were divided into 2 groups of 27 patients each. Both groups were followed up to three years post-implantation.

Results

Cerebrospinal fluid ooze developed in 12 patients, and 2 patients had a cerebrospinal fluid ‘gusher’, one of which had to be explored within 24 hours. After implant use for one year, both groups had similar speech perception scores.

Conclusion

The cerebrospinal fluid gusher in Mondini dysplasia should be anticipated and adequately managed intra-operatively. This study highlights the tailoring of a post-implantation rehabilitation programme according to individual needs.

Keywords

Cochlear ImplantsCerebrospinal Fluid
Type
Main Articles
Information
The Journal of Laryngology & Otology , Volume 135 , Issue 2 , February 2021 , pp. 125 - 129
Copyright
Copyright © The Author(s), 2021. Published by Cambridge University Press

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Footnotes

Dr N M Suri takes responsibility for the integrity of the content of the paper

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