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Personality traits in treated Wilson’s disease determined by means of the Karolinska Scales of Personality (KSP)

Published online by Cambridge University Press:  16 April 2020

K. Portala ,
K. Westermark ,
L. Ekselius  and
L. von Knorring
K. Portala*
Affiliation:
Department of Neuroscience, Psychiatry, Uppsala University Hospital, SE-751 85Uppsala, Sweden
K. Westermark
Affiliation:
Department of Internal Medicine, Uppsala University Hospital, SE-751 85Uppsala, Sweden
L. Ekselius
Affiliation:
Department of Neuroscience, Psychiatry, Uppsala University Hospital, SE-751 85Uppsala, Sweden
L. von Knorring
Affiliation:
Department of Neuroscience, Psychiatry, Uppsala University Hospital, SE-751 85Uppsala, Sweden
*
* Correspondence and reprints. E-mail address: Kamilla.Portala@UASpsyk.uu.se (K. Portala).
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Summary

Objective

The aim was to elucidate the personality traits of patients with treated Wilsonˈs disease (WD) in comparison to healthy volunteers.

Method

Twenty-five WD patients, ten females and 15 males, with a mean age of 35.2 ± 8.3 years completed the Karolinska Scales of Personality (KSP), a self-report inventory comprising 15 separate scales. The results were compared to a control series comprising 200 men and 200 women drawn from the general population.

Results

The patients with treated WD scored significantly lower than the healthy controls on aggressivity-hostility-related scales and the scale measuring Psychic Anxiety. Patients with predominantly hepatic symptoms had the lowest aggressivity-related scores and patients with predominantly neurological symptoms had the lowest Irritability, Guilt and Detachment scores and the highest Impulsiveness and Muscular Tension scores. Both groups scored low on the Somatic Anxiety scale.

Conclusion

The present results illustrate that patients with treated WD have significant deviations in personality traits, especially in aggressivity-hostility-related scales and Psychic Anxiety, compared to healthy controls when investigated by means of a self-report inventory, the KSP. The deviations were not related to age, age at onset or duration of the disease.

Keywords

hepatolenticular degenerationKarolinska scales of personalitypersonality traitsWilson’s disease
Type
Original article
Information
European Psychiatry , Volume 16 , Issue 6 , September 2001 , pp. 362 - 371
Copyright
Copyright © 2001 Éditions scientifiques et médicales Elsevier SAS. All rights reserved

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