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Use of oral budesonide in the management of protein-losing enteropathy due to restrictive cardiomyopathy

Published online by Cambridge University Press:  13 September 2013

Hazım A. Gursu ,
Birgul Varan  and
Ilkay Erdogan
Hazım A. Gursu*
Affiliation:
Department of Paediatric Cardiology, Baskent University, Ankara, Turkey
Birgul Varan
Affiliation:
Department of Paediatric Cardiology, Baskent University, Ankara, Turkey
Ilkay Erdogan
Affiliation:
Department of Paediatric Cardiology, Baskent University, Ankara, Turkey
*
Correspondence to. H. A. Gursu, MD, Department of Paediatric Cardiology, Baskent University, Bahcelievler, Cankaya 06490, Ankara, Turkey. Tel: +90 505 5618799; Fax: +90 312 2237333; E-mail: hagursu@yahoo.com.tr
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Abstract

A 7-year-old male patient who had abdominal swelling and eyelid oedema was diagnosed with restrictive cardiomyopathy. His serum albumin level was 2.3 g/dl. Protein-losing enteropathy due to restrictive cardiomyopathy was diagnosed and oral budesonide was started. His serum albumin level began to rise and ascites and peripheric oedema disappeared. The patient underwent a successful cardiac transplantation and budesonide was stopped. After the heart transplantation, the albumin level decreased to 2.3 g/dl, and therefore it was restarted. When the serum albumin level increased, the budesonide dose was tapered and stopped in 1 month. Budesonide may be an effective drug in patients with protein-losing enteropathy due to heart failure.

Keywords

Protein-losing enteropathyhypoalbuminaemiacardiac transplantation
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 4 , August 2014 , pp. 764 - 766
Copyright
Copyright © Cambridge University Press 2013 

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