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Unique foetal diagnosis of aorto-pulmonary collaterals in right atrial isomerism

Published online by Cambridge University Press:  26 November 2020

Wadi Mawad
Affiliation:
Division of Cardiology, Department of Pediatrics, Montreal Children’s Hospital, MontrealCanada Department of Pediatrics, McGill University, Montreal, Canada
Nathalie Dutil
Affiliation:
Division of Cardiology, Department of Pediatrics, The Labatt Family Heart Centre, The Hospital for Sick Children, Toronto, Canada
Varsha Thakur*
Affiliation:
Division of Cardiology, Department of Pediatrics, The Labatt Family Heart Centre, The Hospital for Sick Children, Toronto, Canada Department of Pediatrics, University of Toronto, Toronto, Canada
*
Author for correspondence: Varsha Thakur, MD, The Hospital for Sick Children, The University of Toronto, 555 University Avenue, Toronto, ON, Canada M5G 1X8. Tel: 416-813-6140; Fax: 416-813-7547. E-mail: Varsha.thakur@sickkids.ca

Abstract

Right atrial isomerism is associated with complex cardiac malformations, particularly single-ventricle lesions; right atrial isomerism is rarely associated with aorto-pulmonary collateral arteries. We report a foetal diagnosis of right atrial isomerism, with an unbalanced atrioventricular septal defect, pulmonary stenosis, total anomalous venous drainage, and significant aorto-pulmonary collaterals diagnosed at 22 weeks’ gestation.

Type
Brief Report
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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