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Transposition of the great arteries and sinus venosus defect with partially anomalous pulmonary venous return: physiological and anatomic considerations

Published online by Cambridge University Press:  06 June 2014

Vijayakumar Raju ,
Rahul Rathod ,
Luis G. Quinonez  and
Christopher W. Baird
Vijayakumar Raju
Affiliation:
Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
Rahul Rathod
Affiliation:
Department of Cardiology, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
Luis G. Quinonez
Affiliation:
Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
Christopher W. Baird*
Affiliation:
Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
*
Correspondence to: C. W. Baird, Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, 300 Longwood Avenue, Bader 273, Boston, MA 02115, United States of America. Tel: 617-355-1914; Fax: 617-730-0214; E-mail: chris.baird@cardio.chboston.org
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Abstract

Transposition of the great arteries is a common congenital heart defect causing cyanosis in neonates, occurring in 0.2 per 1000 live births. It has been reported to occur with other associated congenital heart lesions. However, its association with a superior sinus venosus defect and partially anomalous pulmonary venous return has not been reported. We present a neonate with transposition of the great arteries, superior sinus venosus defect with partially anomalous pulmonary venous return that underwent successful complete neonatal repair, and discuss important physiological and anatomic considerations.

Keywords

Congenital heart diseasetransposition of the great vesselssinus venosus septal defectpartially anomalous pulmonary venous return
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 4 , April 2015 , pp. 787 - 789
Copyright
© Cambridge University Press 2014 

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References

1. Fyler, DC, Buckley, LP, Hellenbrand, WE. Report of the New England regional infant cardiac program. Pediatrics 1990; 65 (Suppl): 375–461.Google Scholar
2. Gontijo, B, Fantini, M, Barbosa, V, Gomes, MV, Gutierrez, C, Vrandecic, M. Surgical repair of transposition of great arteries and total anomalous pulmonary venous return to the coronary sinus (TGA with TAPVR). Eur J Cardiothorac Surg 1994; 8: 391–392.Google Scholar
3. Talwar, S, Rajashekar, P, Reedy, VA, Choudhary, SK, Airan, B. Transposition of great arteries and partial anomalous pulmonary venous drainage. Asian Cardiovasc Thorac Ann 2013; 21: 713–716.CrossRefGoogle ScholarPubMed
4. Grosse-Wortmann, L, Al-Otay, A, Goo, HW, et al. Anatomical and functional evaluation of pulmonary veins in children by magnetic resonance imaging. J Am Coll Cardiol 2007; 49: 993–1002.CrossRefGoogle ScholarPubMed
5. Walker, RE, Mayer, JE, Alexander, ME, Walsh, EP, Berul, CI. Paucity of sinus node dysfunction following repair of sinus venosus defects in children. Am J Cardiol 2001; 87: 1223–1226.CrossRefGoogle ScholarPubMed
6. Van Praagh, S, Carrera, ME, Sanders, SP, Mayer, JE, Van Praagh, R. Sinus venosus defects: unroofing of the right pulmonary veins: anatomic and echocardiographic findings and surgical treatment. Am Heart J 1994; 128: 365–379.Google Scholar
7. Stewart, RD, Bailliard, F, Kelle, AM, et al. Evolving surgical strategy for sinus venosus atrial septal defect: effect on sinus node function and late venous obstruction. Ann Thorac Surg 2007; 84: 1651–1655.Google Scholar